妞嶇墿楂斿収(n猫i)鏅亶瀛樺湪钁楀洓鐢插熀鎴婁簩閰�锛屽畠鏄績閫�(j矛n)妞嶇墿鐢熼暦(zh菐ng)鐨勯噸瑕佸洜绱犱箣涓€锛屽婧愬洓鐢插熀鎴婁簩閰搁€�(j矛n)鍏ユ鐗╅珨鍏�(n猫i)锛屽叿鏈夊収(n猫i)婧愬洓鐢插熀鎴婁簩閰稿悓妯ｇ殑鐢熺悊鍔熻兘銆傚畠涓昏缍�(j墨ng)鐢辫憠鐗�銆佸鏋濄€佽姳銆佺ó瀛愭垨鏋滃(sh铆)閫�(j矛n)鍏ユ鐗╅珨鍏�(n猫i)锛岀劧鍚庡偝灏�(d菐o)鑷崇敓闀�(zh菐ng)娲昏簫鐨勯儴浣嶈捣浣滅敤銆�
鑻辨枃鍚嶇ū(ch膿ng)锛�Tetramethyl glutaric aciduria
鎬� 鐙€锛� 鐐虹櫧鑹茬矇鏈�锛涘懗寰吀锛屾憾浜庢按锛屼笉婧朵簬閱�銆佽嫰
鍒� 瀛� 寮�锛�C6H11NO4
鍚� 閲�锛� 99%
鍒� 瀛� 閲�锛�1461.15
鐔� 榛�(di菐n)锛�205鈩�
鍥涚敳鍩烘垔浜岄吀鎬ц兘锛氬洓鐢插熀鎴婁簩閰稿湪妞嶇墿楂斿収(n猫i)鐨勮泲鐧借唱(zh矛)浠ｈ瑵閬�(gu貌)绋嬩腑鍗犻噸瑕佸湴浣�锛屽弮鑸囧嫊(d貌ng)鐗┿€佹鐗╁拰寰敓鐗╀腑鐨勮ū澶氶噸瑕佸寲瀛�(xu茅)鍙嶆噳(y墨ng)銆�
鍥涚敳鍩烘垔浜岄吀鐗归粸(di菐n)锛氭鐗╅珨鍏�(n猫i)鏅亶瀛樺湪钁楀洓鐢插熀鎴婁簩閰�锛屽畠鏄績閫�(j矛n)妞嶇墿鐢熼暦(zh菐ng)鐨勯噸瑕佸洜绱犱箣涓€锛屽婧愬洓鐢插熀鎴婁簩閰搁€�(j矛n)鍏ユ鐗╅珨鍏�(n猫i)锛屽叿鏈夊収(n猫i)婧愬洓鐢插熀鎴婁簩閰稿悓妯ｇ殑鐢熺悊鍔熻兘銆傚畠涓昏缍�(j墨ng)鐢辫憠鐗�銆佸鏋濄€佽姳銆佺ó瀛愭垨鏋滃(sh铆)閫�(j矛n)鍏ユ鐗╅珨鍏�(n猫i)锛岀劧鍚庡偝灏�(d菐o)鑷崇敓闀�(zh菐ng)娲昏簫鐨勯儴浣嶈捣浣滅敤銆�
鍥涚敳鍩烘垔浜岄吀鑳藉杩呴€熸徊閫忓埌妞嶇墿楂斿収(n猫i)锛屼績閫�(j矛n)绱�(x矛)鑳炵殑鍘熺敓璩�(zh矛)娴佸嫊(d貌ng)鍜岀窗(x矛)鑳炲垎瑁�锛屽姞蹇鐗╂牴鑾栬垏涓嶅畾鏍圭殑鐢熼暦(zh菐ng)閫熷害锛屼娇鑾栦几寮�锛岃憠鐗囨摯(ku貌)澶у帤瀵�(sh铆)锛屽柈鎬х祼(ji茅)瀵�(sh铆)锛屼績閫�(j矛n)鏋滃(sh铆)鐢熼暦(zh菐ng)锛屾敼鍠勫拰鎻愰珮鏋滃(sh铆)鍝佽唱(zh矛)锛屾墦鐮寸ó瀛愪紤鐪�锛屾敼璁婇泴闆勮姳姣旂巼锛屽奖闊块枊(k膩i)鑺辨檪(sh铆)闁�銆佹笡灏戝拰闃叉鑺�銆佹灉鐨勮劔钀�銆�
鍥涚敳鍩烘垔浜岄吀瑕�(ji脿n)鏁堝揩銆佹寔鏁堟湡闀�(zh菐ng)銆佺敤閲忓皯銆佹垚鏈綆銆佹晥鐩婇珮寤ｆ硾鎳�(y墨ng)鐢ㄤ簬杈�(n贸ng)銆佹灄鍦掕棟锛屽叿鍌�寰�(f霉)纭濋厷閳�銆�鑳洪鑴�銆佽悩涔欓吀鐨勬墍鏈夊姛鑳�锛岀敤閲�?j墨)H鐐�寰�(f霉)纭濋厷閳�銆�鑳洪鑴�銆�钀樹箼閰搁垑鐨�50%-60%锛屽氨鑳介仈(d谩)鍒�寰�(f霉)纭濋厷閳�銆�鑳洪鑴�銆�钀樹箼閰搁垑鐨勬墍鏈夊劒(y艒u)榛�(di菐n)鍜屽姛鑳�锛屾垚鐐鸿棩銆佽偉銆佹鑿屽姂鐨勭悊鎯冲鏁堝姂鍜屼績閫�(j矛n)鍔�銆�
鍥涚敳鍩烘垔浜岄吀浣跨敤鏂规硶鍜岀壒榛�(di菐n)锛氬洓鐢插熀鎴婁簩閰稿彲浠ヨ憠闈㈠櫞鏂�銆佽拷鏂�銆佸熀鏂�锛屼娇鐢ㄥ彲鎸夐噺鑸囧熀鑲�銆佸京(f霉)娣疯偉銆佹湁姗�(j墨)鑲�銆佽拷鏂借偉閰嶅悎浣跨敤銆傞爜(y猫)闈㈠櫞鏂芥噳(y墨ng)鐢ㄩ噺鐐�0.1-0.15姣厠/鍗冨厠锛岃拷鏂藉拰鍩烘柦鐐烘瘡鐣�5-8鍏�銆�
鍥涚敳鍩烘垔浜岄吀鐒�(w煤)鑹层€佺劇(w煤)鍛�銆佺劇(w煤)姣掓垚鏈綆鏁堢泭楂�锛屾槸杈�(n贸ng)妤�(y猫)銆佹灄妤�(y猫)銆佸湌钘濈瓑绋(l猫i)鐨勫ソ骞墜鍜屾鐗╃敓闀�(zh菐ng)瑾�(di脿o)绡€(ji茅)鍔戜腑鏈€鐐哄劒(y艒u)鑹殑铏�(h脿o)鐢�(ch菐n)鍝�銆�
鐗瑰垾娉ㄦ剰锛氱敤鍥涚敳鍩烘垔浜岄吀淇冮€�(j矛n)鍋氶亷(gu貌)鍒烘縺鐢熼暦(zh菐ng)鏅�(sh铆)锛屾按鑲ヤ竴瀹氳鍏呰冻銆傝伅(li谩n)绯婚浕瑭�(hu脿) 13838030319 QQ锛�2224277452
